Jornal Vascular Brasileiro
https://www.jvascbras.org/journal/jvb/article/doi/10.1590/1677-5449.009218
Jornal Vascular Brasileiro
Review Article

Algorithm for diagnosis of primary vasculitides

Algoritmo diagnóstico de vasculites primárias

Alexandre Sacchetti Bezerra; Afonso César Polimanti; Rafael Vilhena de Carvalho Fürst; João Antônio Corrêa

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Abstract

Abstract: Primary vasculitides are diseases with a wide variety of anatomical, clinical, radiological, and laboratory presentations. Primary vasculitides are difficult to diagnose because of the complexity of clinical presentation, which may lead to delayed treatment and increased financial costs of workup investigations involving non-essential tests. Our objective in the present study is to create an algorithm that helps diagnosis of Primary vasculitides. The algorithm presented in this article allows fast, simple and cost-effective diagnosis of primary vasculitides using just clinical concepts and a few laboratory tests.

Keywords

algorithms, classification, diagnosis, differential, systemic vasculitis, vasculitis

Resumo

Resumo: As vasculites primárias são doenças que possuem apresentações anatômicas, clínicas, radiológicas e laboratoriais muito distintas. Em virtude da complexidade dos quadros clínicos apresentados, as vasculites primárias são de difícil diagnóstico, o que pode promover um retardo no início da terapêutica, além de aumentar os custos financeiros da investigação propedêutica com exames não essenciais. O objetivo deste estudo foi criar um algoritmo que auxilie o diagnóstico das vasculites primárias. O algoritmo apresentado neste artigo permite a realização de diagnóstico rápido, simples e de baixo custo nas vasculites primárias, com a utilização de alguns conceitos clínicos e poucos exames laboratoriais.
 

Palavras-chave

algoritmos, classificação, diagnóstico diferencial, vasculite sistêmica, vasculite

References

Criado PR, Marques GF, Morita TC, Carvalho JF. Epidemiological, clinical and laboratory profiles of cutaneous polyarteritis nodosa patients: report of 22 cases and literature review. Autoimmun Rev. 2016;15(6):558-63. http://dx.doi.org/10.1016/j.autrev.2016.02.010. PMid:26876385.

Jennette JC, Falk RJ, Bacon PA, et al. 2012 revised International Chapel Hill Consensus Conference Nomenclature of Vasculitides. Arthritis Rheum. 2013;65(1):1-11. http://dx.doi.org/10.1002/art.37715. PMid:23045170.

Alberti-Violetti S, Berti E, Marzano AV. Cutaneous and systemic vasculitides in dermatology: a histological perspective. G Ital Dermatol Venereol. 2018;153(2):185-93. PMid:29368866.

Ramos-Casals M, Stone JH, Cid MC, Bosch X. The cryoglobulinaemias. Lancet. 2012;379(9813):348-60. http://dx.doi.org/10.1016/S0140-6736(11)60242-0. PMid:21868085.

Brandt HR, Arnone M, Valente NY, Criado PR, Sotto MN. Vasculite cutânea de pequenos vasos: etiologia, patogênese, classificação e critérios diagnósticos - Parte I. An Bras Dermatol. 2007;82(5):387-406. http://dx.doi.org/10.1590/S0365-05962007000500002.

Jennette JC, Falk RJ, Andrassy K, et al. Nomenclature of systemic vasculitides. Proposal of an international consensus conference. Arthritis Rheum. 1994;37(2):187-92. http://dx.doi.org/10.1002/art.1780370206. PMid:8129773.

Kallenberg CGM, Brouwer E, Weening JJ, Cohen Tervaert JW. Anti-neutrophil cytoplasmic antibodies: current diagnostic and pathophysiological potential. Kidney Int. 1994;46(1):1-15. http://dx.doi.org/10.1038/ki.1994.239. PMid:7933826.

Burns JC, Glodé MP. Kawasaki syndrome. Lancet. 2004;364(9433):533-44. http://dx.doi.org/10.1016/S0140-6736(04)16814-1. PMid:15302199.

Niederkohr RD, Levin LA. Management of the patient with suspected temporal arteritis a decision-analytic approach. Ophthalmol. 2005;112(5):744-56. http://dx.doi.org/10.1016/j.ophtha.2005.01.031. PMid:15878052.

Mason JC. Takayasu arteritis--advances in diagnosis and management. Nat Rev Rheumatol. 2010;6(7):406-15. http://dx.doi.org/10.1038/nrrheum.2010.82. PMid:20596053.

Serra R, Butrico L, Fugetto F, et al. Updates in pathophysiology, diagnosis and management of Takayasu Arteritis. Ann Vasc Surg. 2016;35:210-25. http://dx.doi.org/10.1016/j.avsg.2016.02.011. PMid:27238990.

Centers for Medicare & Medicaid Services [site da internet]. 2018. [citado 2018 set 28]. www.medicaid.gov

Departamento de Informática do SUS – DATASUS [site da internet]. 2018. [citado 2018 set 28]. www.datasus.gov.br

Banco Central do Brasil [site da internet]. 2018. [citado 2018 set 28]. www.bcb.gov.br

Radu AS, Levi M. Anticorpos contra o citoplasma de neutrófilos. J Bras Pneumol. 2005;31(Suppl 1):s16-20. http://dx.doi.org/10.1590/S1806-37132005000700006.

Radice A, Bianchi L, Sinico RA. Anti-neutrophil cytoplasmic autoantibodies: methodological aspects and clinical significance in systemic vasculitis. Autoimmun Rev. 2013;12(4):487-95. http://dx.doi.org/10.1016/j.autrev.2012.08.008. PMid:22921790.

Lionaki S, Blyth ER, Hogan SL, et al. Classification of antineutrophil cytoplasmic autoantibody vasculitides: the role of antineutrophil cytoplasmic autoantibody specificity for myeloperoxidase or proteinase 3 in disease recognition and prognosis. Arthritis Rheum. 2012;64(10):3452-62. http://dx.doi.org/10.1002/art.34562. PMid:23023777.

Homer RJ. Antineutrophil cytoplasmic antibodies as markers for systemic autoimmune disease. Clin Chest Med. 1998;19(4):627-39, viii. http://dx.doi.org/10.1016/S0272-5231(05)70107-6. PMid:9917957.

Calvo-Rio V, Loricera J, Mata C, et al. Henoch-Schonlein purpura in northern Spain: clinical spectrum of the disease in 417 patients from a single center. Medicine. 2014;93(2):106-13. http://dx.doi.org/10.1097/MD.0000000000000019. PMid:24646467.

Brogan P, Eleftheriou D. Vasculitis update: pathogenesis and biomarkers. Pediatr Nephrol. 2018;33(2):187-98. http://dx.doi.org/10.1007/s00467-017-3597-4. PMid:28785984.

Souza AW. Autoantibodies in systemic vasculitis. Front Immunol. 2015;6:184. PMid:25954277.

Cacoub P, Comarmond C, Domont F, Savey L, Saadoun D. Cryoglobulinemia Vasculitis. Am J Med. 2015;128(9):950-5. http://dx.doi.org/10.1016/j.amjmed.2015.02.017. PMid:25837517.

Ragab G, Hussein MA. Vasculitic syndromes in hepatitis C virus: a review. J Adv Res. 2017;8(2):99-111. http://dx.doi.org/10.1016/j.jare.2016.11.002. PMid:28149646.

Simonetti O, Postacchini V, Offidani A. Cutaneous vasculitis and inflammatory bowel diseases. G Ital Dermatol Venereol. 2015;150(2):233-6. PMid:25830412.

Arora A, Wetter DA, Gonzalez-Santiago TM, Davis MD, Lohse CM. Incidence of leukocytoclastic vasculitis, 1996 to 2010: a population-based study in Olmsted County, Minnesota. Mayo Clin Proc. 2014;89(11):1515-24. http://dx.doi.org/10.1016/j.mayocp.2014.04.015. PMid:24981218.

Carlson JA. The histological assessment of cutaneous vasculitis. Histopathology. 2010;56(1):3-23. http://dx.doi.org/10.1111/j.1365-2559.2009.03443.x. PMid:20055902.

Loricera J, Calvo-Rio V, Mata C, et al. Urticarial vasculitis in northern Spain: clinical study of 21 cases. Medicine. 2014;93(1):53-60. http://dx.doi.org/10.1097/MD.0000000000000013. PMid:24378743.

Neves FS, Moraes JC, Gonçalves CR. Síndrome de Behçet: à procura de evidências. Rev Bras Reumatol. 2006;46(Suppl 1):21-9. http://dx.doi.org/10.1590/S0482-50042006000700005.
 

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