Jornal Vascular Brasileiro
https://www.jvascbras.org/article/doi/10.1590/1677-5449.0065
Jornal Vascular Brasileiro
Case Report

Aortic thrombosis in a patient with a late diagnosis of Behcet's disease

Trombose aórtica em paciente com diagnóstico tardio de Doença de Behçet

Ana Bittencourt Detanico; Marcelo Luiz Brandão; Ly de Freitas Fernandes; Carolina Parreira Ribeiro Camelo; Juliano Ricardo Santana dos Santos

Downloads: 0
Views: 96

Abstract

Behcet's disease is form of systemic vasculitis of unknown etiology. One surprising feature is that arterial involvement is less common in this disease than venous forms, accounting for 1 to 7% of patients. In 7 to 30% of cases the vascular symptoms precede the clinical diagnosis of Behcet. We describe the case of a patient with Thromboangiitis Obliterans who was treated with lumbar sympathectomy and an aortobiiliac bypass. Around 1 year later he was diagnosed with Behcet's disease after presenting with oral ulcers, genital ulcers and scaling lesions on the hands.

Keywords

Behcet Syndrome, arteritis, peripheral arterial disease

Resumo

A Doença de Behçet é uma vasculite sistêmica de etiologia desconhecida. O inusitado é que o acometimento arterial nesta doença é menos comum que o venoso, correspondendo a 1 a 7% dos pacientes. Já os sintomas vasculares precedem o diagnóstico clínico de Behçet em 7 a 30%. Relatamos o caso de um paciente portador de Tromboangeíte Obliterante que foi submetido a simpatectomia lombar e derivação aorto-bi-ilíaca. Após cerca de um ano, diagnosticou-se Doença de Behçet, devido a quadro clínico de úlceras orais, genitais e lesões descamativas nas mãos.

Palavras-chave

Síndrome de Behçet, arterite, doença arterial periférica

References

Kenneth J, Warrington TC, Leslie TC. Vasculitis and other arteriopathies. Rutherford's vascular surgery. 2010:1156-68.

Yurdakul S, Hamuryudan V, Yazici H. Behçet syndrome. Curr Opin Rheumatol.. 2004;16(1):38-42.

Treudler R, Orfanos CE, Zouboulis CC. Twenty-eight cases of juvenile-onset Adamantiades-Behçet disease in Germany. Dermatology.. 1999;199(1):15-9.

Karincaoglu Y, Borlu M, Toker SC,. Demographic and clinical properties of juvenile-onset Behçet's disease: a controlled multicenter study. J Am Acad Dermatol.. 2008;58(4):579-84.

Yang SS, Park KM, Park YJ,. Peripheral arterial involvement in Behcet's disease: an analysis of the results from a Korean referral center. Rheumatol Int.. 2013;33(8):2101-8.

Melikoglu M, Kural-Seyahi E, Tascilar K, Yazici H. The unique features of vasculitis in Behçet's syndrome. Clin Rev Allergy Immunol.. 2008;35(1-2):40-6.

Calamia KT, Schirmer M, Melikoglu M. Major vessel involvement in Behçet disease. Curr Opin Rheumatol.. 2005;17(1):1-8.

Sarica-Kucukoglu R, Akdag-Kose A, KayabalI M, et al. Vascular involvement in Behçet's disease: a retrospective analysis of 2319 cases. Int J Dermatol.. 2006;45(8):919-21.

Ames PRJ, Steuer A, Pap A, Denman AM. Thrombosis in Behçet's disease: a retrospective survey from a single UK centre. Rheumatology (Oxford).. 2001;40(6):652-5.

Düzgün N, Ateş A, Aydintuğ OT, Demir O, Olmez U. Characteristics of vascular involvement in Behçet's disease. Scand J Rheumatol.. 2006;35(1):65-8.

Jayachandran NV, Rajasekhar L, Chandrasekhara PK, Kanchinadham S, Narsimulu G. Multiple peripheral arterial and aortic aneurysms in Behcet's syndrome: a case report. Clin Rheumatol.. 2008;27(2):265-7.

Kural-Seyahi E, Fresko I, Seyahi N, et al. The long-term mortality and morbidity of Behçet syndrome: a 2-decade outcome survey of 387 patients followed at a dedicated center. Medicine (Baltimore).. 2003;82(1):60-76.

Calamia KT, Wilson FC, Icen M, Crowson CS, Gabriel SE, Kremers HM. Epidemiology and clinical characteristics of Behçet's disease in the US: a population-based study. Arthritis Rheum.. 2009;61(5):600-4.

Robenshtok E, Krause I. Arterial involvement in Behçet's disease--the search for new treatment strategies. Isr Med Assoc J.. 2004;6(3):162-3.

5de7f48c0e8825eb1ce31d42 jvb Articles
Links & Downloads

J Vasc Bras

Share this page
Page Sections