Jornal Vascular Brasileiro
https://www.jvascbras.org/article/doi/10.1590/1677-5449.180121
Jornal Vascular Brasileiro
Case Report

Tratamento endovascular da doença de Behçet: relato de caso

Endovascular treatment for Behçet’s disease: a case report

Sergio Quilici Belczak; Ingredy Tavares da Silva; Gustavo Garcia Marques; Letícia Flores Copetti; Vanessa Stefaniak; Gustavo Gomes Quintas; Kaique Bernardo Uchimura

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Resumo

Resumo: A doença de Behçet (DB) é uma vasculite multissistêmica de etiologia desconhecida. O acometimento cardiovascular é bem descrito na literatura, sendo que a principal causa de morte na DB é secundária a complicações aneurismáticas. Relata-se aqui o caso de um paciente portador de DB com aneurisma de aorta abdominal reincidente, o qual foi corrigido por meio de endoprótese customizada. O tratamento ideal para portadores de DB ainda é bastante controverso e desafiador, tendo em vista as dificuldades técnicas e as recidivas frequentes. A intervenção endovascular apresenta-se como uma alternativa viável e consideravelmente menos mórbida do que a cirurgia convencional.

Palavras-chave

Síndrome de Behçet, procedimentos endovasculares, stents, aneurisma

Abstract

Abstract: Behçet’s disease (BD) is a multisystemic vasculitis of unknown etiology. Cardiovascular involvement has been thoroughly described in the literature and the major cause of death in BD is secondary to aneurysm complications. In this case report, a patient with BD presented with a recurrent abdominal aortic aneurysm, which was corrected using a custom-made endoprosthesis. The optimal treatment for patients with BD remains highly controversial and challenging because of technical difficulties and frequent recurrence. Endovascular intervention seems to be a feasible alternative with considerably less morbidity than conventional surgery.
 

Keywords

Behçet syndrome, endovascular procedures, stents, aneurysm

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