Jornal Vascular Brasileiro
https://www.jvascbras.org/article/doi/10.1590/1677-5449.200017
Jornal Vascular Brasileiro
Case Report

Rotura de aneurisma de artéria poplítea em paciente clinicamente diagnosticado com síndrome de Marfan

Ruptured popliteal artery aneurysm in a patient with a clinical diagnosis of Marfan syndrome

Gabriel Paiva Duarte; Jorge Ribeiro da Cunha Júnior

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Resumo

Resumo: A artéria poplítea é o principal local para a ocorrência de aneurismas periféricos. Suas formas de apresentação agudas são potencialmente ameaçadoras à viabilidade do membro e à vida, dentre as quais destacamos a sua rotura. Apesar de ser um evento raro, sua rotura demanda rápida proposta de intervenção para satisfatório desfecho terapêutico. O tratamento padrão-ouro é o cirúrgico convencional e se dá pela interposição de veia safena magna. Trabalhos feitos nas últimas décadas vêm encontrando associações entre a síndrome de Marfan e aneurismas periféricos. Este relato apresenta um caso de um aneurisma de artéria poplítea esquerda roto tratado com sucesso em um paciente de 82 anos diagnosticado clinicamente como portador de síndrome de Marfan previamente desconhecida.

Palavras-chave

artéria poplítea, aneurisma roto, síndrome de Marfan

Abstract

The popliteal artery is the main site of occurrence of peripheral aneurysms. Acute presentations constitute a potential threat to limb viability and to life, especially in the event of rupture. Rupture is a rare event, but one that demands an immediate intervention decision to achieve a satisfactory treatment outcome. The gold standard treatment is conventional surgery, effecting repair by interposition of a great saphenous vein graft. Studies conducted in recent decades have found associations between Marfan Syndrome and peripheral aneurysms. This report presents a case of a ruptured left popliteal artery aneurysm successfully treated in an 82-year-old patient clinically diagnosed with previously unknown Marfan syndrome.

Keywords

popliteal artery; ruptured aneurysm; Marfan syndrome.

References

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Submitted date:
02/25/2020

Accepted date:
05/28/2020

5f8f22f00e8825c72c0c62b5 jvb Articles

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