Jornal Vascular Brasileiro
https://www.jvascbras.org/article/doi/10.1590/S1677-54492006000100015
Jornal Vascular Brasileiro
Case Report

Doença de Behçet cursando com trombose de veia cava superior

Behçet's disease presenting with superior vena cava thrombosis

Otacílio Figueiredo da Silva Júnior; Ricardo Henrique de Sousa Araújo; Eutília Andrade Medeiros Freire; Ronaldo Rangel Travassos Júnior; Thiago Emanuel Rodrigues Cavalcante; Tarcísio José Pinheiro Lucena; Norberto de Castro Nogueira Neto; Alessandra Vanessa de Albuquerque Melo

Downloads: 0
Views: 106

Resumo

A trombose venosa é o principal acometimento do sistema vascular na doença de Behçet, sendo uma complicação freqüente na evolução clínica dessa patologia, e está mais associada ao sexo masculino. Os autores relatam o caso de uma paciente do sexo feminino que apresentou início da doença há 3 anos com úlceras orais, além de úlceras genitais, e que vem cursando com episódios recorrentes de trombose venosa, sendo a primeira uma trombose venosa profunda no membro inferior direito; a segunda, de jugular interna esquerda; e, por último, uma trombose da veia cava superior.

Palavras-chave

Doença de Behçet, trombose venosa, síndrome da veia cava superior

Abstract

Venous thrombosis is the main hazard to the vascular system in Behçet's disease. It is a frequent complication throughout the clinical evolution of this illness, which is more associated with the male gender. The authors report the case of a female patient with disease onset 3 years ago, showing oral and genital ulcers presenting with recurring episodes of venous thrombosis. The first one was a deep venous thrombosis in the right leg; the second was in the left internal jugular vein; and finally a superior vena cava thrombosis.

Keywords

Behçet's disease, venous thrombosis, superior vena cava syndrome

References

Evaluation of diagnostic (classification) criteria in Behcet's disease: towards internationally agreed criteria. Br J Rheumatol. 1992;31:229-308.

Radke PW, Schwarz ER, Groesdonk H, Graf J, Janssens U. Thrombosis in Behcet's disease: report of a case followed by a systematic review using the methodology of the evidence-based medicine. J Thromb Thrombolysis. 2001;11:137-41.

Al-Otaibi LM, Porter SR, Poate TW. Behcet's disease: a review. J Dent Res. 2005;84:209-22.

Dervis E, Geyik N. Sensitivity and specificity of different diagnostic criteria for Behcet's disease in a group of Turkish patients. J Dermatol. 2005;32:266-72.

Cecil RL, Goldman L, Bennet JC. Doenças músculo-esqueléticas e do tecido conjuntivo: doença de Behçet. Tratado de medicina interna. 2001:1716-7.

Hirohata S, Kikuchi H. Behcet's disease. Arthritis Res Ther. 2003:139-46.

Leiba M, Ehrenfeld M. Behcet's disease: current therapeutic perspectives. Curr Treat Options Cardiovasc Med. 2005;7:139-48.

Castelli P, Caronno R, Pifaretti G. Endovascular treatment for superior vena cava obstruction in Behcet disease. J Vasc Surg. 2005;41:548-51.

Houman MH, Ben Ghorbel I, Khiari Ben Salah I, Lamloum M, Ben Ahmed M, Miled M. Deep vein thrombosis in Behcet's disease. Clin Exp Rheumatol. 2001;19:S48-50.

Ames PR, Steuer A, Pap A, Denman AM. Thrombosis in Behcet's disease: a retrospective survey from a single UK centre. Reumathology. 2001;40:652-5.

Carreño Pérez L. Enfermedad de Behçet. An Med Interna. 2001;18:401-4.

Kontogiannis V, Powell RJ. Behcet's disease. Postgrad Med J. 2000;76:629-37.

Chaloupka K, Baglivo E, Hofer M. Thrombose des sinus veineux cerébraux dans la maladie: description d'un cas et revue de la litérature. Klin Monatsbl Augenheilkd. 2003;220:186-8.

Wechsler B, Sbai A, Du-Boutin LT, Duhaut P, Dormont D, Piette JC. Manifestations neurologiques de la maladie de Behçet. Rev Neurol. 2002;158:926-33.

Cemri M, Erkan A, Ozdemir M, Cengel A. Behcet's disease with a large and free right atrial thrombus. Eur J Echocardiogr. 2002;3:233-5.

Houman H, Lamloum M, Ben Ghorbel I, Khiari-Ben Salah I, Miled M. Thromboses caves dans la maladie de Behçet. Ann Med Interne. 1999;150:587-90.

Ehrlich GE. Behcet disease and the emergence of thalidomide. Ann Intern Med. 1998;128:494-5.

Hamuryudan V, Mat C, Saip S. Thalidomide in the treatment of the mucocutaneous lesions of the Behcet syndrome: a randomized, double-blind, placebo-controlled trial. Ann Intern Med. 1998;128:443-50.

Demiroglu H, Yalcin S, Buyukasik Y. Mucocutaneous lesions in the Behcet syndrome. Ann Intern Med. 1998;129:836.

Vidaller Palacín A, Robert Olalla J, Sanuy Jiménez B. Tratamiento de la enfermedad de Behçet. An Med Interna. 2002;19:594-8.

5dea4a2e0e8825b51a2afa9e jvb Articles
Links & Downloads

J Vasc Bras

Share this page
Page Sections