Jornal Vascular Brasileiro
https://www.jvascbras.org/article/doi/10.1590/S1677-54492007000200016
Jornal Vascular Brasileiro
Case Report

Malformação de veia cava inferior e trombose venosa profunda: fator de risco de trombose venosa em jovens

Inferior vena cava malformation and deep venous thrombosis: a risk factor of venous thrombosis in the young

Renan Roque Onzi; Luiz Francisco Costa; Regis Fernando Angnes; Luciano Amaral Domingues; Paulo Moraes; Leandro Armani Scaffaro; Carolina Mancuzo Stapenhorst

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Resumo

A ausência da veia cava inferior, alteração no processo de formação embriológica que ocorre entre a sexta e a oitava semanas de gestação, é uma rara anomalia congênita. Porém, recentemente foi confirmada como sendo um fator de risco importante para o desenvolvimento de trombose venosa profunda, especialmente em jovens. Apresentamos um caso de trombose em veias cava inferior, ilíacas, femorais e poplíteas num jovem de 16 anos com agenesia de um segmento de veia cava infra-renal e veia renal esquerda retroaórtica.

Palavras-chave

Veia cava inferior, trombose venosa profunda

Abstract

Absence of inferior vena cava, caused by aberrant development within the sixth to eighth weeks of gestation, is a rare congenital anomaly. However, it has been recently confirmed as a major risk factor for the development of deep venous thrombosis, especially in young patients. We report a case of inferior vena cava, iliac, femoral and popliteal vein thrombosis in a 16-year-old patient with inferior vena cava agenesis and retroaortic left renal vein.

Keywords

Inferior vena cava, deep venous thrombosis

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