Jornal Vascular Brasileiro
https://www.jvascbras.org/article/doi/10.1590/S1677-54492012000100013
Jornal Vascular Brasileiro
Case Report

Correção endovascular de aneurisma de aorta abdominal e artéria ilíaca comum esquerda em paciente com hemofilia C grave

Endovascular repair of abdominal aortic aneurysm and left common iliac artery in a patient with severe hemophilia C

Sergio Quilici Belczak; Igor Rafael Sincos; Ricardo Aun; Boulanger Mioto Neto; Manoel Lobato; Fernando Saliture; Alex Ledermain

http://dx.doi.org/10.1590/S1677-54492012000100013 J Vasc Bras, vol.11, n1, p.73-76, 2012
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Resumo

A deficiência do fator XI, também conhecida como hemofilia C, é uma doença hematológica hereditária rara, que se manifesta clinicamente com hemorragia persistente após cirurgias, traumas, menorragias e extrações dentárias. Neste artigo, relatou-se a correção endovascular de um paciente com aneurisma de aorta e de artéria ilíaca comum esquerda em um paciente portador de deficiência major do fator XI (atividade do fator XI inferior a 20%). O procedimento foi realizado com sucesso, com o manuseio do distúrbio da coagulação por meio da infusão de plasma fresco no pré-operatório imediato e no pós-operatório, e controle laboratorial da coagulação do paciente.

Palavras-chave

deficiência do fator XI, aneurisma aórtico, procedimentos endovasculares

Abstract

Factor XI deficiency, also known as hemophilia C, is a rare hereditary blood disease that manifests with persistent bleeding after surgery, trauma, menorrhagia, and dental extractions. This article reports an endovascular repair of a patient diagnosed with an aortic and left common iliac aneurysm, with severe factor XI deficiency (factor XI activity below 20%). The procedure was successfully performed with management of the coagulation disorder by preoperative and postoperative infusion of plasma and laboratory control of the coagulation.

Keywords

factor XI deficiency, aortic aneurysm, endovascular procedures

References

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