Jornal Vascular Brasileiro
https://www.jvascbras.org/journal/jvb/article/doi/10.1590/1677-5449.001016
Jornal Vascular Brasileiro
Case Report

Tratamento endovascular de aneurisma de tronco braquiocefálico em paciente com síndrome de Ehlers-Danlos tipo IV

Endovascular treatment of an aneurysm of the brachiocephalic trunk in a patient with Ehlers-Danlos syndrome type IV

Sergio Quilici Belczak, Rafael Kogan Klajner, Lara Cote Ogawa, Laís Leite Lucato, Bruna Stecca Zeque, Felipe Basso de Macedo, Ingredy Tavares da Silva, Luís Felipe Atihe

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Resumo

A síndrome de Ehlers-Danlos é uma doença genética que acarreta alteração na síntese de colágeno, causando extrema fragilidade do tecido conjuntivo. Tal fragilidade predispõe a uma série de doenças vasculares, como dissecções, aneurismas e pseudoaneurismas. Os autores relatam o histórico de um indivíduo de 19 anos com aneurisma de tronco braquiocefálico que foi submetido ao tratamento endovascular com implante de stents revestidos. O caso evoluiu com complicação do sítio de punção, que também foi tratada em caráter de emergência pela técnica endovascular com o implante de stent revestido.

Palavras-chave

aneurisma; tronco braquiocefálico; síndrome de Ehlers-Danlos

Abstract

Ehlers-Danlos syndrome is a genetic disease that results in abnormalities of collagen synthesis, causing extremely fragile connective tissue. This fragility predisposes patients to a series of vascular disorders, such as dissections, aneurysms and pseudoaneurysms. The authors describe the case of a 19-year-old patient with an aneurysm of the brachiocephalic trunk who was treated endovascularly by placement of covered stents. The case progressed with complications at the puncture site, which was also treated on an emergency basis, using endovascular techniques with a covered stent.

Keywords

aneurysm; brachiocephalic trunk; Ehlers-Danlos syndrome

References

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